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KMID : 1037820170060020041
Journal of Pain and Autonomic Disorders
2017 Volume.6 No. 2 p.41 ~ p.45
Chronic Autonomic Failure with Reduced Cardiac Uptake on 123I-Methyliodobenzylguanidine Scintigraphy
Na Seung-Hee

Lee Eek-Sung
Lee Tae-Kyeong
Abstract
Chronic autonomic failure by involvement of peripheral autonomic pathway often occurs as a complication of diseases such as diabetes, amyloidosis, inflammatory neuropathy, and etc. Contrasting those conditions where autonomic dysfunction as a consequence of peripheral neuropathy, pure autonomic failure (PAF) is a rare neurodegenerative disorder involving primarily peripheral autonomic pathway. We experienced a patient with severe autonomic failure who showed sympathetic denervation in 123I-Methyliodobenzylguanidine scintigraphy. We discuss the clinical features and differential diagnosis of PAF with review of literatures.
KEYWORD
Pure autonomic failure, Orthostatic hypotension, Myocardial scintigraphy
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